Thoracoabdominal aortic aneurysm repair in Marfan syndrome: how we do it.
نویسندگان
چکیده
Department of Cardiothoracic and Vascular Surgery, McGovern Medical School at the University of Texas Health Science Center at Houston (UTHealth), Houston, TX, USA; Memorial Hermann Heart & Vascular Institute, Houston, TX, USA Correspondence to: Rana O. Afifi, MD. Department of Cardiothoracic and Vascular Surgery, McGovern Medical School at UTHealth, 6400 Fannin St., Suite #2850, Houston, TX 77030, USA. Email: [email protected].
منابع مشابه
Hybrid Thoracic Endovascular Aortic Repair for Intercostal Patch Aneurysm after Thoracoabdominal Aortic Replacement.
We report a case of hybrid thoracic endovascular aortic repair for intercostal patch aneurysm after thoracoabdominal aortic replacement. Eighteen years ago, a 63-year-old woman with Marfan syndrome had undergone thoracoabdominal aortic replacement with reimplantation of the intercostal artery in an island fashion. Follow-up computed tomography (CT) revealed a remaining intercostal patch aneurys...
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Aneurysms associated with inherited connective tissue disorders (CTD) constitute a specific but important issue in thoracoabdominal aortic aneurysm (TAAA) surgery. In this respect, Marfan syndrome and Ehlers-Danlos syndrome (EDS) type IV represent the most significant disorders causing aneurysmal dilatation of the thoracic aorta. Marfan syndrome typically causes aortic root dilatation, aortic v...
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Cerebrospinal fluid (CSF) drainage is a routinely used adjunct in operation of thoracoabdominal aortic aneurysm (TAAA), which may reduce the incidence of perioperative paraplegia by improving spinal cord perfusion. Neurological complications of CSF drainage have been reported, possibly due to excessive CSF drainage, and acute subdural hematoma (SDH) in particular may lead to catastrophic compli...
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The advent of multi-gene panel genetic testing and the discovery of new syndromic and non-syndromic forms of connective tissue disorders have established thoracic aortic aneurysms as a genetically mediated disease. Surgical results in patients with Marfan syndrome (MFS) provide an important benchmark for this patient population. Prophylactic aortic root surgery prevents acute dissection and has...
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Marfan syndrome is a well-described autosomal dominant connective tissue disorder with a constellation of anatomic characteristics including aortic degeneration as a result of the spontaneous mutation of the fibrillin gene, FBN1. Whereas life-threatening dissection and ascending aneurysmal rupture have been thoroughly documented in the literature, aneurysms of the abdominal aorta and those pres...
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ورودعنوان ژورنال:
- Annals of cardiothoracic surgery
دوره 6 6 شماره
صفحات -
تاریخ انتشار 2017